WTF ........................................................................

Discussion in 'The Howard Stern Show' started by Shithead, Jan 18, 2016.

  1. Shithead

    Shithead Well-Known Member

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    Colombian teen with rare premature ageing disease surpasses her 13-year life expectancy to celebrate traditional 15th birthday party with family and friends
    By Dailymail.com Reporter
    Published: 17:18 EST, 17 January 2016 | Updated: 17:22 EST, 17 January 2016



    Like so many young teenage girls, little Magali Gonzalez Sierra loves dancing, music, glitter, pink and make-up.
    But unlike her friends, this teenager is trapped in the body of a 90-year-old, and has already exceeded her life expectancy of 13.
    Magali, from Colombia, is one of a few young people around the world to suffer from Hutchinson-Gilford progeria syndrome, a fatal genetic condition characterized by an appearance of accelerated ageing in children. It means her parents live in fear that one day she won't wake up.
    However, though she cannot walk and requires intense medication, this month Magali defied doctors' expectations to reach her 15th birthday.
    And it made her quinceañera even more special.
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    Magali Gonzalez Sierra has defied doctors' expectations by living past the age of 13 to turn 15 years old
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    The little girl suffers from Hutchinson-Gilford progeria syndrome, which gives children an aged appearance
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    On Saturday, Magali celebrated her quinceañera - the Latin American equivalent of a Sweet Sixteen
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    Here, like all other girls in her village who turn 15, she has her make-up done for the party later
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    She poses for a selfie with a family member after having a wig and make-up and crown put on
    A quinceañera is the Latin American equivalent of a Sweet Sixteen, celebrated on a girl's 15th birthday.
    Dressed as a princess, the birthday girl has a big party with all her friends to celebrate 'coming of age'.
    Few girls are more thankful for their quinceañera than Magali.

    Speaking to Colombian news site Publimetro, her mother Sofia, 35, said: 'Magali wants to be 15. She told me she wants her party; that even though she doesn't dance, she wants us to dance. She wants balloons and celebrations and that people come.'
    While there are different forms of progeria, the classic type is Hutchinson-Gilford Progeria Syndrome, which was named after English doctors Dr Jonathan Hutchinson and Dr Hastings Gilford who first described it in 1886 and 1897 respectively.
    HGPS is caused by a mutation in the gene called LMNA.
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    Magali is carried by her father Jose Eider Gonzalez before her birthday party in El Cabuyal, Colombia
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    Here Magali is dressed by her mother Sofia Sierra and Colombia's fashion designer Miguel Becerra
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    Friends gather around Magali who has bunches of flowers on her lap
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    A quinceañera is the Latin American equivalent of a Sweet Sixteen, celebrated on a girl's 15th birthday. Few girls are more thankful for their quinceanera than Magali
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    A cart carrying Colombian Magali Gonzalez Sierra, 15, and her family arriver to her 15th birthday party in El Cabuyal, department of Valle del Cauca, Colombia
    The LMNA gene produces the Lamin A protein, which is the structural scaffolding that holds the nucleus of a cell together.
    Researchers now believe that the defective Lamin A protein makes the nucleus unstable.
    That cellular instability appears to lead to the process of premature aging in Progeria.
    Although they are born looking healthy, children with progeria begin to display many characteristics of accelerated ageing at around 18-24 months of age.
    Progeria signs include growth failure, loss of body fat and hair, aged-looking skin, stiffness of joints, hip dislocation, generalized atherosclerosis, cardiovascular (heart) disease and stroke.
    The children have a remarkably similar appearance, despite differing ethnic backgrounds.
    Children with progeria die of heart disease at an average age of 13 or 14 years.
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    Magali poses for a photo with her parents Jose (second right) and Sofia (left), and her sister Mayerli (right)
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    This is a picture of Sofia holding little Magali when she was six months old
     
  2. FrstTimeLngTme

    FrstTimeLngTme Well-Known Member

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    Happy birthday to her
     
  3. a mysterious man

    a mysterious man Well-Known Member

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    That's not creepy at all at 5:15 in the morning.
     
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  4. Shortwave98

    Shortwave98 A-Number 1 Banned User

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    Guilty! Oh wait...
     
  5. Margos

    Margos Sprinkles are for winners.

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    That disease is so heartbreaking. Glad she got to celebrate.
     
  6. Skipnoid

    Skipnoid Lick Me!

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  7. lilbuddy67

    lilbuddy67 A man with breath-taking anger management issues Banned User

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  8. Tickle Shits

    Tickle Shits Special Needs Typist. Gold

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    [​IMG]
     
  9. reno

    reno VIP Extreme Gold

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    For those who think their life is hard, look at that poor child.
     
  10. MrWarmth

    MrWarmth ADORABLE DEPLORABLE Gold

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    She should count her blessings she wasn't born with two heads.
     
  11. boognishstern

    boognishstern Well-Known Member

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    she likes madonna. she's a club kid.
     
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  12. boognishstern

    boognishstern Well-Known Member

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    all joking aside, that's really fucking sad. hope she had a fun night.
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  13. Honkey Donkey

    Honkey Donkey Well-Known Member

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    She was great on Strangers With Candy .


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  14. Honkey Donkey

    Honkey Donkey Well-Known Member

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    Oops wrong person . Happy birthday to her . And many more to come .
     
  15. peterfonda

    peterfonda Well-Known Member

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    Seeing a child suffering like that puts all of our petty bullshit into perspective, doesn't it? People like her make me wonder - does God put people like her on Earth to make the rest of us try to appreciate what we have and make us better people?